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Last reviewed dd mmm yyyy. Last edited dd mmm yyyy
Treatment is largely preventive - avoid inducing agents.
Glucose loading and haematin infusions have largely been unsuccessful as have phlebotomy and chloroquine for the skin lesions.
During acute attacks, IV infusion of haem arginate 3mg/kg (a maximum of 250mg) once daily for four consecutive days is recommended (1).
Treatment with opiates may be required during acute attacks. Symptomatic treatment for other complaints is recommended. Seizures may be treated with IV lorazepam or clonazepam (1).