Management
The management of Von Gierke disease aims to prevent episodes of fasting hypoglycaemia, keeping blood glucose above 4 mmol/l (1).
The most effective approaches include:
- continuous glucose infusion:
- intravenous
- via nasogastric tube
- via gastrostomy tube
- regular ingestion of uncooked corn starch
Reference:
- Parikh N. Glycogen Storage Disease Type I. Treasure Island (FL): StatPearls Publishing. 2025 Jan.
Create an account to add page annotations
Annotations allow you to add information to this page that would be handy to have on hand during a consultation. E.g. a website or number. This information will always show when you visit this page.